This gene encodes a mitochondrial protein that is involved in an early step of vitamin B metabolism.

In other diseases, defects in nuclear genes lead to dysfunction of mitochondrial proteins.

HSP60, as a mitochondrial protein, has been shown to be involved in stress response as well.

Some mutations affect the gene MFN2, which codes for a mitochondrial protein.

These genes each provide instructions for making part of an enzyme complex called mitochondrial trifunctional protein.

As the name suggests, mitochondrial trifunctional protein contains three enzymes that each perform a different function.

Uncoupling protein 1 (UCP1), a unique brown fat mitochondrial protein, is also positive.

All mitochondrial proteins would then be imported into the mitochondria.

Researchers have identified a group of mitochondrial proteins, the absence of which allows other protein groups to stabilise the genome.

StAR is a mitochondrial protein that is rapidly synthesized in response to stimulation of the cell to produce steroid.